Search on:
PYRUVATE CARBOXYLASE
Descriptors Found:
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DeCS
Descriptor
English
:
Pyruvate Carboxylase
Descriptor
Spanish
:
Piruvato Carboxilasa
Descriptor
Portuguese
:
Piruvato Carboxilase
Tree Number:
D08.811.464.257.500
Definition
English
:
A biotin-dependent enzyme belonging to the ligase
family
that catalyzes the addition of
CARBON DIOXIDE
to pyruvate. It is occurs in both
plants
and
animals
. Deficiency of this enzyme causes severe psychomotor retardation and
ACIDOSIS
, LACTIC in infants. EC 6.4.1.1.
Entry Combination - descr/qualif
English
:
Pyruvate Carboxylase
/
deficiency
use
Pyruvate Carboxylase Deficiency Disease
See Related
English
:
Pyruvate Carboxylase Deficiency Disease
History Note
English
:
74
Allowable Qualifiers
English
:
AD
administration & dosage
AE
adverse effects
AN
analysis
AI
antagonists & inhibitors
BI
biosynthesis
BL
blood
CF
cerebrospinal fluid
CS
chemical synthesis
CH
chemistry
CL
classification
CT
contraindications
DU
diagnostic use
DE
drug effects
EC
economics
GE
genetics
HI
history
IM
immunology
IP
isolation & purification
ME
metabolism
PK
pharmacokinetics
PD
pharmacology
PH
physiology
PO
poisoning
RE
radiation effects
SE
secretion
ST
standards
SD
supply & distribution
TU
therapeutic use
TO
toxicity
UL
ultrastructure
UR
urine
Record Number:
12203
Unique Identifier:
D011766
Occurrence in VHL
:
Similar:
DeCS
CID-10
SciELO
LILACS
LIS